Чернодробни усложнения при ß-таласемия

  • Деница Кофинова
Keywords: таласемия, черен дроб, усложнения

Abstract

Бета-таласемията е едно от най-честите автозомно-рецесивни заболявания. С подобряване на хелаторното лечение и навлизането на неинвазивните методики за оценка и проследяване на желязното натрупването, качеството и продължителността на живот на пациентите с ß-таласемия значително се подобри. Черният дроб е първия таргетен орган, който се уврежда, директно и индиректно. В настоящия обзор се разглеждат най-честите чернодробни усложнения като развитие на фиброза и цироза, методи за оценка на желязното натоварване, хронични вирусни хепатити, развитие на хепатоцелуларен карцином и холелитиаза.

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Published
2023-09-13
How to Cite
1.
Кофинова Д. Чернодробни усложнения при ß-таласемия. Редки болести и лекарства сираци [Internet]. 2023Sep.13 [cited 2024Nov.11];14(1):5-. Available from: https://journal.raredis.org/index.php/RBLS/article/view/172
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